What is the surgery for Hirschsprung disease?
For most people, Hirschsprung’s disease is treated with surgery to bypass or remove the part of the colon that’s lacking nerve cells. There are two ways this can be done: a pull-through surgery or an ostomy surgery.
What is Hirschsprung disease Slideshare?
1. Hirschsprung’s disease Ushneesh Banerjee Intern Malda Medical College & Hospital. 2. Introduction • Hirschprung’s Disease, aslo known as Congenital Megacolon or Aganglionic Megacolon an abnormality in which certain nerve fibres are absent in segments of the bowel, resulting in severe bowel obstruction.
What is a Levelling colostomy?
A leveling colostomy is formed at diagnosis for decompression of the dilated bowel proximal to the aganglionic segment. After an appropriate time interval, a colon pull-through is performed with either simultaneous or subsequent ostomy closure.
Can Hirschsprung disease be treated without surgery?
Although most children with Hirschsprung disease do not need ostomy surgery, a child sick from Hirschsprung disease may need ostomy surgery to get better before undergoing the pull-through procedure. This gives the inflamed areas of the intestine time to heal.
What are the types of Hirschsprung disease?
There are two main types of Hirschsprung disease, known as short-segment disease and long-segment disease, which are defined by the region of the intestine lacking nerve cells. In short-segment disease, nerve cells are missing from only the last segment of the large intestine (colon).
Is Hirschsprung disease painful?
Children with this disorder are missing nerve cells in all or part of the large intestine. Without these nerve cells, stool can’t move forward through the large intestine. This can cause constipation, swelling, pain, and infection.
What is the cause of Hirschsprung’s disease?
It’s not clear what causes Hirschsprung’s disease. It sometimes occurs in families and might, in some cases, be associated with a genetic mutation. Hirschsprung’s disease occurs when nerve cells in the colon don’t form completely. Nerves in the colon control the muscle contractions that move food through the bowels.
What is the pathophysiology of Hirschsprung disease?
Hirschsprung disease results from the absence of enteric neurons within the myenteric and submucosal plexus of the rectum and/or colon. Enteric neurons are derived from the neural crest and migrate caudally with the vagal nerve fibers along the intestine.
What are the complications of Hirschsprung’s disease?
Overall, the most common complications are anastomotic leakage and stricture formation in 5%-15%, wound infection in 10%, intestinal obstruction in 5%, pelvic abscess in 5%, and reoperation in 5% of patients.
What to expect after surgery for Hirschsprung’s?
Immediately following successful surgery, many children with Hirschsprung’s disease have diarrhea for weeks. Diarrhea may break down sensitive skin under the diaper, and the child recognizes intense pain after each bowel movement.
What is another name for Hirschsprung disease?
Congenital aganglionic megacolon (Hirschsprung disease).
Can you poop with Hirschsprung disease?
Most children treated surgically for Hirschsprung disease have an excellent outcome. Most can pass stool normally and have no lasting complications. A few kids might continue to have symptoms, including constipation and bowel control problems.